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D80.0* |
Hereditary hypogammaglobulinemia
Autosomal recessive agammaglobulinemia (Swiss type)
X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency)
|
D80.1 |
Nonfamilial hypogammaglobulinemia
Agammaglobulinemia with immunoglobulin-bearing B-lymphocytes
Common variable agammaglobulinemia [CVAgamma]
Hypogammaglobulinemia NOS
|
D80.2* |
Selective deficiency of immunoglobulin A [IgA] |
D80.3* |
Selective deficiency of immunoglobulin G [IgG] subclasses |
D80.4* |
Selective deficiency of immunoglobulin M [IgM] |
D80.5* |
Immunodeficiency with increased immunoglobulin M [IgM] |
D80.6* |
Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia |
D80.7* |
Transient hypogammaglobulinemia of infancy |
D80.8 |
Other immunodeficiencies with predominantly antibody defects
Kappa light chain deficiency
|
D80.9 |
Immunodeficiency with predominantly antibody defects, unspecified |
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|
D81.0* |
Severe combined immunodeficiency [SCID] with reticular dysgenesis |
D81.1* |
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers |
D81.2* |
Severe combined immunodeficiency [SCID] with low or normal B-cell numbers |
D81.4 |
Nezelof's syndrome |
D81.5* |
Purine nucleoside phosphorylase [PNP] deficiency
|
D81.6* |
Major histocompatibility complex class I deficiency
Bare lymphocyte syndrome
|
D81.7* |
Major histocompatibility complex class II deficiency |
D81.82* |
Activated Phosphoinositide 3-kinase Delta Syndrome [APDS] |
D81.89* |
Other combined immunodeficiencies |
D81.9* |
Combined immunodeficiency, unspecified
Severe combined immunodeficiency disorder [SCID] NOS
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Excludes: ataxia telangiectasia [Louis-Bar] (G11.3)
|
D82.0* |
Wiskott-Aldrich syndrome
Immunodeficiency with thrombocytopenia and eczema
|
D82.1* |
Di George's Syndrome
Pharyngeal pouch syndrome
Thymic alymphoplasia
Thymic aplasia or hypoplasia with immunodeficiency
|
D82.2 |
Immunodeficiency with short-limbed stature |
D82.3 |
Immunodeficiency following hereditary defective response to Epstein-Barr virus
X-linked lymphoproliferative disease
|
D82.4* |
Hyperimmunoglobulin E [IgE] syndrome |
D82.8 |
Immunodeficiency associated with other specified major defects |
D82.9 |
Immunodeficiency associated with major defect, unspecified |
|
|
D83.0* |
Common variable immunodeficiency with predominant abnormalities of B-cell numbers
and function
|
D83.1* |
Common variable immunodeficiency with predominant immunoregulatory T-cell disorders |
D83.2* |
Common variable immunodeficiency with autoantibodies to B- or T-cells |
D83.8* |
Other common variable immunodeficiencies |
D83.9* |
Common variable immunodeficiency, unspecified |
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D84.9 |
Immunodeficiency, unspecified |
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G11.3* |
Cerebellar ataxia with defective DNA repair Ataxia telangiectasia |
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G61.81* |
Chronic Inflammatory demyelinating polyneuritis
Chronic inflammatory demyelinating polyneuropathy
Chronic inflammatory demyelinating polyradiculoneuropathy
Polyneuropathy (multiple nerve disorder)
Polyneuropathy, chronic inflammatory demyelinating
Polyradiculoneuropathy, chronic inflammatory demyelinating
Polyradiculoneuropathy, inflammatory demyelinating
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